Provider: Silverchair Database: AmericanMedicalAssociation Content: text/plain; charset="UTF-8" TY - JOUR AU - Balaji, Seshadri AU - Rychik, Jack AU - Moore, Jeremy P. T1 - Fontan Junctional Rhythm—Innocent Bystander or Silent Killer? PY - 2024 Y1 - 2024/04/24 DO - 10.1001/jamacardio.2024.0689 JO - JAMA Cardiology JA - JAMA Cardiol SN - 2380-6583 AB - The Fontan operation for single-ventricle hearts alleviates cyanosis but creates a hemodynamically fragile circulation. Without a right ventricle, pulmonary flow is driven by venous pressure, making it the limiting factor for cardiac output. Furthermore, the obligatory rise in central venous pressure leads to hepatic and splanchnic congestion. Consequently, long-term consequences include Fontan failure (FF) and hepatic congestion resulting in Fontan-associated liver disease (FALD). Y2 - 5/20/2024 UR - https://doi.org/10.1001/jamacardio.2024.0689 ER -