@article{10.1001/jamacardio.2024.0689, author = {Balaji, Seshadri and Rychik, Jack and Moore, Jeremy P.}, title = "{Fontan Junctional Rhythm—Innocent Bystander or Silent Killer?}", journal = {JAMA Cardiology}, year = {2024}, month = {04}, abstract = "{The Fontan operation for single-ventricle hearts alleviates cyanosis but creates a hemodynamically fragile circulation. Without a right ventricle, pulmonary flow is driven by venous pressure, making it the limiting factor for cardiac output. Furthermore, the obligatory rise in central venous pressure leads to hepatic and splanchnic congestion. Consequently, long-term consequences include Fontan failure (FF) and hepatic congestion resulting in Fontan-associated liver disease (FALD).}", issn = {2380-6583}, doi = {10.1001/jamacardio.2024.0689}, url = {https://doi.org/10.1001/jamacardio.2024.0689}, eprint = {/journals/jamacardiology/articlepdf/2817828/jamacardiology\_balaji\_2024\_vp\_240002\_1712935232.33609.pdf}, }